Small intestine necrosis in catastrophic antiphospholipid syndrome: A rare and severe case

Tobias K. Christiansen, Anna Christine Nilsson, Gunvor I. Madsen, Anne Voss*

*Corresponding author for this work

Research output: Contribution to journalJournal articleResearchpeer-review

Abstract

Catastrophic antiphospholipid syndrome (CAPS) is a multisystem autoimmune disease with widespread thrombotic events. In this case report, we present a young man with primary antiphospholipid syndrome (PAPS) admitted to the hospital with abdominal pain and vomiting. Abdominal computed tomography showed pneumoperitoneum and acute explorative laparotomy revealed small intestinal necrosis indicating small vessel thrombosis without involvement of large intestine. “Triple therapy” was initiated after surgery and the patient was treated in an intensive care unit for 72 days before being discharged to a rehabilitation clinic. A review of the literature regarding CAPS affecting small intestine shows it is extremely rare and may be associated with higher mortality.

Original languageEnglish
JournalLupus
Volume31
Issue number6
Pages (from-to)754-758
ISSN0961-2033
DOIs
Publication statusPublished - May 2022

Bibliographical note

Publisher Copyright:
© The Author(s) 2022.

Keywords

  • antiphospholipid syndrome
  • catastrophic antiphospholipid syndrome
  • plasma exchange
  • small intestine necrosis

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