Laryngeal neurofibromatose hos et ni måneder gammelt barn

Neurofibroma of the larynx is a very rare condition. A nine month-old boy presented with airway obstruction due to a plexiform neurofibroma of the larynx. It also involved the proximal part of trachea and hypopharynx. Surgical excision was not a possibility. A tracheotomy was performed in order to secure the airways. The patient was doing well afterwards and has been followed with an MRI scan twice a year. Though neurofibroma of the larynx is rare, it should be considered when diagnosing of children with airway obstruction. Long-term follow-up is essential due to risk of malignant transformation.